Dosing and uses of MSUD Analog
Adult dosage forms and strengths
Not indicated
Pediatric dosage forms and strengths
Dependent upon age, body weight, and medical condition; use under medical supervision
Intake is adjusted to maintain normal growth and development
Per 100 g of powder, MSUD Analog provides 13 g of protein equivalent
Suggested uses of MSUD Analog
Unflavored, isoleucine-, leucine- and valine-free powdered infant formula for the dietary management of maple syrup urine disease (MSUD)
MSUD Analog adverse (side) effects
Studies not conducted
Warnings
Contraindications
None
Cautions
Not for parenteral use
Not intended as the sole source of nutrition
Must be consumed in conjunction with a whole protein source (e.g. breast milk or standard infant formula) in quantities prescribed by a dietitian or physician to meet isoleucine, leucine and valine requirements and ensure normal growth
Pregnancy and lactation
Pregnancy category: N/A, for pediatric use only
Lactation: N/A, for pediatric use only
Pregnancy categories
A: Generally acceptable. Controlled studies in pregnant women show no evidence of fetal risk.
B: May be acceptable. Either animal studies show no risk but human studies not available or animal studies showed minor risks and human studies done and showed no risk.
C: Use with caution if benefits outweigh risks. Animal studies show risk and human studies not available or neither animal nor human studies done.
D: Use in LIFE-THREATENING emergencies when no safer drug available. Positive evidence of human fetal risk.
X: Do not use in pregnancy. Risks involved outweigh potential benefits. Safer alternatives exist.
NA: Information not available.
Pharmacology of MSUD Analog
Kinetic info: studies not conducted
Osmolality
15% w/v: 377 mOsm/kg
Mechanism of action
N/A
