Educational Content: This article is for informational purposes only and does not constitute medical advice. Always consult a healthcare provider for diagnosis and treatment.

Definition of Histiocytosis, lipid

Medically reviewed by Min Clinic Staff | Updated: January 2026

Histiocytosis, lipid: A form of histiocytosis that affects lipid (fat) storage. Also known as Niemann- Pick disease, Erdheim-Chester disease.